Volume : 9, Issue : 5, May - 2020

E-ACCESSIBILITY FOR STUDENTS WITH DISABILITIES

Dr. Sampurna Guha

Abstract :

Von Hippel–Lindau (VHL) disease is a rare, autosomal dominantly inherited multisystem disorder characterized by development of a variety of benign and malignant tumors. We report a rare case of Von Hippel Lindau Syndrome and discuss about the Clinical Presentation and Neurosurgical Management of the patient with Von Hippel Lindau Syndrome. Due to a combination of robust radiologic and clinical screening and advanced surgical techniques, the morbidity and mortality of patients with VHL disease has been reduced significantly. A Multidisciplinary team approach is important in screening for VHL disease.